External and internal appearance of hepatorenal polycystic disease.

A fifty four years old male was followed in nephrology clinic since 1999 for hepatorenal polycystic disease. The patient was referred for abdominal distension with postprandial fullness. Family history of hepatorenal polycystic disease in the father, grandmother and a paternal aunt. On physical examination there was a globular abdomen, with multiple irregular masses, which imprint on the abdominal wall, and tenderness are hard and painless (Fig. 1). In additional studies, laboratory tests displayed normal renal and liver function. We performed a CT scan that showed an important hepatomegaly, in which virtually the entire liver parenchyma was replaced by multiple images of rounded, hypodense, cystic appearance and different sizes, in conjunction with the polycystic disease, producing a significant mass effect on gastric cavity, the duodenal and intestinal loops, which were displaced towards the pelvic region. Both kidneys were enlarged with multiple bilateral cortical cysts of various sizes (Fig 2). External and internal appearance of hepatorenal polycystic disease